{"id":414,"date":"2022-05-09T08:15:27","date_gmt":"2022-05-09T11:15:27","guid":{"rendered":"https:\/\/mktpatricia.rbmkt.com.br\/?p=414"},"modified":"2025-06-02T13:30:27","modified_gmt":"2025-06-02T16:30:27","slug":"tipos-mais-graves-da-atrofia-muscular-espinhal-ame","status":"publish","type":"post","link":"https:\/\/patriciacrippa.com.br\/en\/tipos-mais-graves-da-atrofia-muscular-espinhal-ame\/","title":{"rendered":"More severe types of Spinal Muscular Atrophy (SMA)"},"content":{"rendered":"<div data-elementor-type=\"wp-post\" data-elementor-id=\"414\" class=\"elementor elementor-414\" data-elementor-post-type=\"post\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-72853f6 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"72853f6\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-019b3c7\" data-id=\"019b3c7\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a342c67 elementor-widget elementor-widget-text-editor\" data-id=\"a342c67\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Do you know the most serious types of AME?<\/p>\n<p><a style=\"font-family: var( --e-global-typography-text-font-family ), Sans-serif; font-weight: var( --e-global-typography-text-font-weight ); background-color: #ffffff; font-size: 1rem;\" href=\"https:\/\/www.instagram.com\/p\/CRovyxAAcyr\/\" target=\"_blank\" rel=\"noopener\">Na hist\u00f3ria natural da Atrofia Muscular Espinhal, existem 5 subtipos<\/a>&nbsp;que variam com a idade do in\u00edcio dos sintomas at\u00e9 a capacidade funcional m\u00e1xima do indiv\u00edduo.<\/p>\n<p>Sendo assim, a AME tipo 0 (ou 1A) e a tipo 1 s\u00e3o as mais graves entre todas, e aqui eu explico a voc\u00eas o porqu\u00ea.<\/p>\n<p>\ud83d\udd39 In SMA Type 0, symptoms still appear in prenatal care, the most common being:<\/p>\n<p>\u27a1Low fetal movement;<br>\u27a1Severe muscle weakness<br>\u27a1Absence of reflexes;<br>\u27a1Severe heart and respiratory failure.<\/p>\n<p>\ud83d\udd39 Already in individuals with SMA Type 1, which corresponds to almost 60 % of cases of the disease, symptoms appear until the sixth month of life and include:<\/p>\n<p>\u27a1Muscle weakness;<br>\u27a1Difficulty to support the neck;<br>\u27a1Difficulty swallowing;<br>\u27a1Respiratory problems, usually requiring the use of ventilation support;<br>\u27a1 Crying and weak cough.<\/p>\n<p>Esse conte\u00fado sobre a&nbsp;<a href=\"https:\/\/patriciacrippa.com.br\/en\/a-atrofia-muscular-espinhal-ame-e-uma-doenca-genetica\/\" target=\"_blank\" rel=\"noopener\">Spinal Muscular Atrophy<\/a>&nbsp;foi \u00fatil para voc\u00ea? Compartilhe esse post com outras pessoas. \ud83d\ude0a<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>","protected":false},"excerpt":{"rendered":"<p>Voc\u00eas conhecem os tipos mais graves de AME? Na hist\u00f3ria natural da Atrofia Muscular Espinhal, existem 5 subtipos&nbsp;que variam com a idade do in\u00edcio dos sintomas at\u00e9 a capacidade funcional m\u00e1xima do indiv\u00edduo. Sendo assim, a AME tipo 0 (ou 1A) e a tipo 1 s\u00e3o as mais graves entre todas, e aqui eu explico [&hellip;]<\/p>","protected":false},"author":1,"featured_media":415,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[26,10],"tags":[27,28,30,31,29,20],"class_list":["post-414","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-atrofia-muscular-espinhal","category-fisioterapia-pediatrica","tag-ame","tag-atrofia-muscular-espinhas","tag-tipo-1","tag-tipo-2","tag-tipos-atrofia-muscular","tag-tratamento-escoliose-infantil"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.1.1 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>AME, conhe\u00e7a os tipos mais graves - Dra. Patricia Crippa<\/title>\n<meta name=\"description\" content=\"J\u00e1 se questionou sobre o que est\u00e1 por tr\u00e1s da causa da Atrofia Muscular Espinhal (AME)? 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